CT abdominal imaging findings in patients with sickle cell disease: acute vaso-occlusive crisis, complications, and chronic sequelae

Abdom Radiol (NY). 2016 Dec;41(12):2524-2532. doi: 10.1007/s00261-016-0890-9.

Abstract

Sickle cell disease (SCD) is the most prevalent hemoglobinopathy. Survival in patients with SCD has improved over the past few decades. These patients experience a lifetime of repeated acute pain crises, which are thought to result from sickling and microvascular occlusions; acute abdominal pain is common. Moreover, repeated crises often lead to organ dysfunction, such as asplenia, hepatic failure, and renal failure. The spleen, liver, biliary system, kidneys, and gastrointestinal tract can all be affected. Patients may undergo CT to further direct clinical management. We review the spectrum of CT imaging findings of abdominal manifestations in patients with SCD, from the acute microvascular occlusive pain crisis to the potential complications and chronic sequelae.

Keywords: Abdominal pain; Ischemia; Microvascular; Sickle cell disease; Vaso-occlusive crisis.

Publication types

  • Review

MeSH terms

  • Abdominal Pain / diagnostic imaging
  • Abdominal Pain / etiology
  • Acute Disease
  • Anemia, Sickle Cell / complications*
  • Anemia, Sickle Cell / diagnostic imaging*
  • Chronic Disease
  • Disease Progression
  • Gastrointestinal Diseases / diagnostic imaging
  • Gastrointestinal Diseases / etiology
  • Humans
  • Radiography, Abdominal / methods*
  • Tomography, X-Ray Computed / methods*
  • Vascular Diseases / diagnostic imaging
  • Vascular Diseases / etiology