Tricuspid atresia associated with aortopulmonary window: diagnostic and therapeutic dilemmas

Cardiol Young. 2017 Apr;27(3):580-583. doi: 10.1017/S1047951116001499. Epub 2016 Sep 29.


The association of tricuspid atresia with aortopulmonary window is exceptionally rare. We report a patient with tricuspid atresia, normally related great arteries, non-restrictive ventricular septal defect, and no pulmonary stenosis (type IC) with an aortopulmonary window who underwent successful initial surgical palliation. The unique anatomical feature of this case, other than the presence of the aortopulmonary window, was the absence of pulmonary stenosis at the level of either the ventricular septal defect or the pulmonary valve. All other reported cases have described some degree of restriction of anterograde pulmonary flow due to pulmonary stenosis or atresia.

Keywords: Tricuspid atresia; aortopulmonary window; staged surgical palliation.

Publication types

  • Case Reports

MeSH terms

  • Abnormalities, Multiple*
  • Aortography
  • Aortopulmonary Septal Defect / diagnosis*
  • Aortopulmonary Septal Defect / surgery
  • Cardiac Catheterization
  • Cardiac Surgical Procedures / methods*
  • Echocardiography
  • Humans
  • Infant, Newborn
  • Male
  • Tricuspid Atresia / diagnosis*
  • Tricuspid Atresia / surgery