Abstract
Mowat-Wilson syndrome is a rare congenital syndrome involving multiple system abnormalities. The most consistently present components include facial deformity, mental retardation, and Hirschsprung disease. We report the anesthetic management of a case of Mowat-Wilson syndrome, with a difficult airway, who underwent Duhamel's procedure and colostomy closure.
Keywords:
Anesthesia; Difficult airway; MWS; Mowat-Wilson syndrome.
Copyright © 2016 Elsevier Inc. All rights reserved.
MeSH terms
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Airway Management / instrumentation
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Airway Management / methods*
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Anesthesia, General / instrumentation
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Anesthesia, General / methods*
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Child, Preschool
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Colon / surgery
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Digestive System Surgical Procedures
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Facies
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Hirschsprung Disease / complications*
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Hirschsprung Disease / surgery*
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Humans
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Intellectual Disability / complications*
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Intellectual Disability / surgery*
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Intubation, Intratracheal / instrumentation
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Intubation, Intratracheal / methods*
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Laryngeal Masks
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Laryngoscopy / instrumentation
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Laryngoscopy / methods*
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Male
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Microcephaly / complications*
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Microcephaly / surgery*
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Patient Positioning