Difficult airway in Mowat-Wilson syndrome

J Clin Anesth. 2016 Nov:34:151-3. doi: 10.1016/j.jclinane.2016.04.001. Epub 2016 May 3.

Abstract

Mowat-Wilson syndrome is a rare congenital syndrome involving multiple system abnormalities. The most consistently present components include facial deformity, mental retardation, and Hirschsprung disease. We report the anesthetic management of a case of Mowat-Wilson syndrome, with a difficult airway, who underwent Duhamel's procedure and colostomy closure.

Keywords: Anesthesia; Difficult airway; MWS; Mowat-Wilson syndrome.

Publication types

  • Case Reports

MeSH terms

  • Airway Management / instrumentation
  • Airway Management / methods*
  • Anesthesia, General / instrumentation
  • Anesthesia, General / methods*
  • Child, Preschool
  • Colon / surgery
  • Digestive System Surgical Procedures
  • Facies
  • Hirschsprung Disease / complications*
  • Hirschsprung Disease / surgery*
  • Humans
  • Intellectual Disability / complications*
  • Intellectual Disability / surgery*
  • Intubation, Intratracheal / instrumentation
  • Intubation, Intratracheal / methods*
  • Laryngeal Masks
  • Laryngoscopy / instrumentation
  • Laryngoscopy / methods*
  • Male
  • Microcephaly / complications*
  • Microcephaly / surgery*
  • Patient Positioning

Supplementary concepts

  • Mowat-Wilson syndrome