Absence of septum pellucidum and polymicrogyria: a forme fruste of the porencephalic syndrome

Clin Neuropathol. 1989 Jul-Aug;8(4):174-8.

Abstract

Two cases are presented of absence of the septum pellucidum associated with bilateral polymicrogyria. In one case a circumscribed, completely enclosed cavity was present in the white matter of one cerebral hemisphere, different in structure from typical prenatal porencephaly. It is suggested that these cases represent a "forme fruste" of the syndrome of absent septum, bilateral porencephaly, polymicrogyria and heterotopia and may be ascribed to a similar, if less severe, encephaloclastic process of debatable etiology, operating around the midterm of pregnancy.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Adult
  • Brain / abnormalities*
  • Female
  • Hemiplegia / pathology
  • Humans
  • Intellectual Disability / pathology
  • Male
  • Septum Pellucidum / abnormalities*
  • Syndrome