Polyglandular autoimmune syndrome type III with a prevalence of cutaneous features

Clin Exp Dermatol. 2017 Jan;42(1):61-63. doi: 10.1111/ced.12984. Epub 2016 Nov 13.

Abstract

Polyglandular autoimmune syndrome (PAS) is the name given to a group of autoimmune disorders of the endocrine glands. PAS type III (PAS III) comprises several autoimmune diseases (autoimmune thyroiditis, immune-mediated diabetes mellitus, pernicious anaemia, vitiligo, alopecia areata and many others) and is subdivided into four subcategories. We report the case of a 52-year-old woman with autoimmune thyroiditis, vitiligo, alopecia areata, psoriasis and lichen sclerosus, suggesting a clinical diagnosis of PAS IIIC with a singular prevalence of cutaneous features.

Publication types

  • Case Reports

MeSH terms

  • Alopecia Areata / complications*
  • Alopecia Areata / diagnosis
  • Anemia, Pernicious / complications
  • Anemia, Pernicious / diagnosis
  • Autoantibodies / immunology
  • Biopsy
  • Diabetes Mellitus, Type 1 / complications
  • Diabetes Mellitus, Type 1 / diagnosis
  • Diagnosis, Differential
  • Female
  • Humans
  • Lichen Sclerosus et Atrophicus / complications*
  • Lichen Sclerosus et Atrophicus / diagnosis
  • Middle Aged
  • Polyendocrinopathies, Autoimmune / complications*
  • Polyendocrinopathies, Autoimmune / diagnosis
  • Polyendocrinopathies, Autoimmune / immunology
  • Prevalence
  • Skin / pathology*
  • Thyroiditis, Autoimmune / complications
  • Thyroiditis, Autoimmune / diagnosis
  • Ultrasonography
  • Vitiligo / complications*
  • Vitiligo / diagnosis

Substances

  • Autoantibodies