Spontaneous rupture of chorioretinal coloboma in an 8-year-old child is treated by temporal fascia graft

J AAPOS. 2017 Feb;21(1):73-75. doi: 10.1016/j.jaapos.2016.08.015. Epub 2016 Nov 16.


We report the rare case of an 8-year-old boy with spontaneous scleral perforation secondary to an isolated congenital chorioretinal coloboma. Visual acuity was 20/200 and examination revealed severe hypotony with subcapsular cataract, complete exudative retinal detachment, hypotonous optic nerve swelling, and hypotony retinal fold. In the temporal periphery, there was a chorioretinal coloboma with a central full-thickness defect. The scleral defect was successfully treated with an autologous temporalis fascia graft. One year later, and after cataract surgery, visual acuity had improved to 20/20, with normal intraocular pressure.

Publication types

  • Case Reports

MeSH terms

  • Child
  • Choroid / abnormalities*
  • Coloboma / diagnosis*
  • Coloboma / surgery
  • Fascia / transplantation
  • Humans
  • Intraocular Pressure / physiology
  • Magnetic Resonance Imaging
  • Male
  • Retina / abnormalities*
  • Rupture, Spontaneous
  • Scleral Diseases / diagnosis*
  • Scleral Diseases / surgery
  • Visual Acuity / physiology