Appendiceal mucoceles (AMs) infrequently arise from an underlying malignancy. Treatment has progressed toward a less aggressive approach over time; they can be managed by appendectomy-only unless pathology reveals malignancy. The ultimate goal of management is to prevent AM rupture, avoiding the syndrome of pseudomyxoma peritonei.
Keywords: Appendiceal mucinous neoplasm; appendix; mucinous cystadenoma; mucocele; pseudomyxoma peritonei.