The Surgical Repair of a Hyperimmunoglobulin E Syndrome Associated Ascending Aortic Aneurysm

Ann Thorac Surg. 2017 Jan;103(1):e65-e67. doi: 10.1016/j.athoracsur.2016.06.021.

Abstract

Hyperimmunoglobulin E syndrome (HIES) is an immunodeficiency disorder that manifests itself by affecting more than one system. Arterial aneurysms are among the significant complications associated with HIES. Surgical procedures for patients with such aneurysms are uncommon. In this study, we aim to present the case and surgical repair of a male child who was previously diagnosed with HIES and presented with rapidly expanding ascending aortic aneurysm.

Publication types

  • Case Reports

MeSH terms

  • Aortic Aneurysm, Thoracic / diagnosis
  • Aortic Aneurysm, Thoracic / etiology
  • Aortic Aneurysm, Thoracic / surgery*
  • Child
  • Echocardiography
  • Humans
  • Job Syndrome / complications*
  • Job Syndrome / surgery
  • Male
  • Tomography, X-Ray Computed
  • Vascular Surgical Procedures / methods*