Endovascular Treatment of Congenital External Carotid-Jugular Fistula: Case Report and Review of the Literature

Vasc Endovascular Surg. 2017 Jul;51(5):316-319. doi: 10.1177/1538574417702777. Epub 2017 Apr 11.


Congenital vascular malformation (CVM) between the external carotid artery and the internal jugular vein is a rare disease, it originates as a consequence of arrested development during various stages of embryogenesis. The natural history of CMVs is progressive growth, it can remain clinically silent until it progresses causing local swelling accompanied by symptoms and signs of arteriovenous shunting, mass effect, ischemic insult with ulceration of skin or bleeding. In literature only few cases of CMVs have been reported, therefore there is still no consensus about the correct surgical approach to this pathology. We report an uncomplicated case of CVMs in a 15-year-old female successfully treated with coils embolization. To our knowledge, this is the eighth reported case in the literature review.

Keywords: coils embolization; congenital malformations; endovascular embolization.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Adolescent
  • Angiography
  • Arteriovenous Fistula / diagnostic imaging
  • Arteriovenous Fistula / therapy*
  • Balloon Occlusion
  • Carotid Artery, External / abnormalities*
  • Carotid Artery, External / diagnostic imaging
  • Embolization, Therapeutic* / instrumentation
  • Endovascular Procedures* / instrumentation
  • Female
  • Humans
  • Jugular Veins / abnormalities*
  • Jugular Veins / diagnostic imaging
  • Magnetic Resonance Imaging
  • Radiography, Interventional
  • Treatment Outcome