Spontaneous evisceration of umbilical hernia in a patient with congenital nephrotic syndrome

J Pak Med Assoc. 2017 May;67(5):799-801.


Congenital nephrotic syndrome is a term used to describe a condition in babies who develop severe proteinuria and hypoalbuminaemia within their first three months of life. They generally have oedema and ascites from birth which, because of increased intra-abdominal pressure, can result in an umbilical hernia. The report presents a five-month old infant with congenital nephrotic syndrome who had spontaneous umbilical hernia rupture with evisceration. The approach to umbilical hernias is usually conservative, but in selected cases elective surgery may be indicated.

Keywords: Umblical Hernia, Evisceration, Nephrotic Syndrome..

Publication types

  • Case Reports

MeSH terms

  • Colon
  • Edema / etiology
  • Female
  • Hernia, Umbilical / etiology
  • Hernia, Umbilical / surgery*
  • Humans
  • Infant
  • Intestine, Small
  • Nephrotic Syndrome / complications*
  • Rupture, Spontaneous / surgery*

Supplementary concepts

  • Nephrosis, congenital