Rare association between spinal dural arteriovenous fistulas and dysraphisms: Report of two cases and review of the literature with a focus on pitfalls in diagnosis and treatment

Interv Neuroradiol. 2017 Oct;23(5):458-464. doi: 10.1177/1591019917714636. Epub 2017 Jul 4.

Abstract

Spinal vascular malformations are uncommon yet important spinal pathologies commonly classified in congenital and acquired lesions. Spinal lipomas consist of three subtypes: intramedullary lipomas, lipomyelo(meningo)celes and lipomas of the filum. Although the association of spinal arteriovenous malformations (AVM) with other congenital anomalies is well known, the coexistence of dural arteriovenous fistulas (AVF) and tethered spinal cord is exceptionally rare and only eight cases have been reported. We present two cases from our institution and speculate on the possible origin of such a rare but insidious association. We review the current literature with a focus on possible pitfalls in diagnosis and treatment.

Keywords: Spinal dural arteriovenous fistula; dysraphism; endovascular treatment; lipoma.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Arteriovenous Malformations / diagnosis*
  • Arteriovenous Malformations / surgery*
  • Central Nervous System Vascular Malformations / diagnosis*
  • Central Nervous System Vascular Malformations / surgery*
  • Female
  • Humans
  • Magnetic Resonance Imaging
  • Male
  • Middle Aged
  • Spinal Cord / blood supply*
  • Young Adult