Airway stenting in a child with spondyloepiphyseal dysplasia congenita: 13-Year survival

Int J Pediatr Otorhinolaryngol. 2017 Aug:99:13-16. doi: 10.1016/j.ijporl.2017.05.008. Epub 2017 May 22.


We describe the case of a boy with spondyloepiphyseal dysplasia congenita. At birth, he experienced severe respiratory distress necessitating tracheotomy. Endoscopy done because mechanical ventilation failed to resolve desaturations disclosed severe tracheo-bronchomalacia. A Polyflex silicone stent was placed in the trachea (replaced by Y-Dumon stent) and 2 Palmaz metallic stents in the mainstem bronchi (overlapped with 2 Jomed stents 5 years later). Airway stenting guaranteed a suitable respiratory status and allowed a child who was expected to die at birth, to reach 13.5 years old in good conditions.

Keywords: Airway; Bronchial stents; Pediatric; Spondyloepiphyseal dysplasia congenita.

Publication types

  • Case Reports

MeSH terms

  • Airway Obstruction
  • Bronchi / surgery
  • Child
  • Child, Preschool
  • Humans
  • Male
  • Osteochondrodysplasias / congenital*
  • Osteochondrodysplasias / surgery
  • Silicones
  • Stents / adverse effects*
  • Trachea / surgery


  • Silicones

Supplementary concepts

  • Spondyloepiphyseal dysplasia, congenita