Pancreas Transplantation Is Feasible in Donors With Shprintzen-Goldberg Syndrome

Transplant Proc. 2017 Oct;49(8):1883-1884. doi: 10.1016/j.transproceed.2017.06.024.

Abstract

Shprintzen-Goldberg syndrome (SGS) is an autosomal dominant connective tissue disorder. To date, this report is the first account of a successful pancreas transplantation from an SGS donor. The similarity of the outcomes from previous year-on-year pancreas transplantations at the same center demonstrates promising results. Increasing awareness of the utilization of donors with SGS may promote expansion of center-specific criteria for organ acceptance. Therefore, every consideration should be given for use of organs from donors with this genetic abnormality because there is no evidence to suggest poorer allograft viability.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Adult
  • Arachnodactyly*
  • Blood Glucose / analysis
  • Craniosynostoses*
  • Diabetes Mellitus, Type 1 / surgery
  • Diabetic Nephropathies / surgery
  • Female
  • Humans
  • Kidney Transplantation
  • Male
  • Marfan Syndrome*
  • Pancreas Transplantation*
  • Tissue Donors*

Substances

  • Blood Glucose

Supplementary concepts

  • Shprintzen Golberg craniosynostosis