Left atrial outflow obstruction in double-outlet right atrium

Asian Cardiovasc Thorac Ann. 2018 Jan;26(1):50-53. doi: 10.1177/0218492317736962. Epub 2017 Oct 8.

Abstract

We describe an unusual case of partial atrioventricular septal defect with malalignment of the septum primum to the left atrium with respect to the ventricular septum, committing the tricuspid valve to both ventricles (double-outlet right atrium). Abnormal attachment of the septum primum to the lateral aspect of mitral annulus resulted in left atrial outflow obstruction. The patient underwent successful surgical correction.

Keywords: Abnormalities; Endocardial cushion defects; Heart atria; Heart defects; Heart septal defects; congenital; multiple.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Atrial Function, Left*
  • Cardiac Surgical Procedures
  • Echocardiography, Transesophageal
  • Female
  • Heart Atria / abnormalities*
  • Heart Atria / diagnostic imaging
  • Heart Atria / physiopathology
  • Heart Atria / surgery
  • Heart Septal Defects, Ventricular / complications*
  • Heart Septal Defects, Ventricular / diagnostic imaging
  • Heart Septal Defects, Ventricular / physiopathology
  • Heart Septal Defects, Ventricular / surgery
  • Hemodynamics*
  • Humans
  • Recovery of Function
  • Treatment Outcome

Supplementary concepts

  • Partial atrioventricular canal