Amyloid β synaptotoxicity is Wnt-PCP dependent and blocked by fasudil

Alzheimers Dement. 2018 Mar;14(3):306-317. doi: 10.1016/j.jalz.2017.09.008. Epub 2017 Oct 19.

Abstract

Introduction: Synapse loss is the structural correlate of the cognitive decline indicative of dementia. In the brains of Alzheimer's disease sufferers, amyloid β (Aβ) peptides aggregate to form senile plaques but as soluble peptides are toxic to synapses. We previously demonstrated that Aβ induces Dickkopf-1 (Dkk1), which in turn activates the Wnt-planar cell polarity (Wnt-PCP) pathway to drive tau pathology and neuronal death.

Methods: We compared the effects of Aβ and of Dkk1 on synapse morphology and memory impairment while inhibiting or silencing key elements of the Wnt-PCP pathway.

Results: We demonstrate that Aβ synaptotoxicity is also Dkk1 and Wnt-PCP dependent, mediated by the arm of Wnt-PCP regulating actin cytoskeletal dynamics via Daam1, RhoA and ROCK, and can be blocked by the drug fasudil.

Discussion: Our data add to the importance of aberrant Wnt signaling in Alzheimer's disease neuropathology and indicate that fasudil could be repurposed as a treatment for the disease.

Keywords: Alzheimer's disease; Amyloid; DAAM1; Dickkopf-1; Fasudil; Planar cell polarity; ROCK; Synapse; Synaptotoxicity; Wnt.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • 1-(5-Isoquinolinesulfonyl)-2-Methylpiperazine / analogs & derivatives*
  • 1-(5-Isoquinolinesulfonyl)-2-Methylpiperazine / pharmacokinetics
  • 1-(5-Isoquinolinesulfonyl)-2-Methylpiperazine / pharmacology
  • Amyloid beta-Peptides / metabolism*
  • Animals
  • Cells, Cultured
  • Cerebral Cortex / drug effects
  • Cerebral Cortex / metabolism
  • Cerebral Cortex / pathology
  • Dose-Response Relationship, Drug
  • Female
  • Intercellular Signaling Peptides and Proteins / metabolism
  • Male
  • Mice
  • Neuroprotective Agents / pharmacokinetics
  • Neuroprotective Agents / pharmacology*
  • Nootropic Agents / pharmacokinetics
  • Nootropic Agents / pharmacology*
  • Primary Cell Culture
  • RNA, Messenger / metabolism
  • Rats
  • Synapses / drug effects
  • Synapses / metabolism*
  • Synapses / pathology
  • Wnt Signaling Pathway* / drug effects
  • Wnt Signaling Pathway* / physiology

Substances

  • Amyloid beta-Peptides
  • Intercellular Signaling Peptides and Proteins
  • Neuroprotective Agents
  • Nootropic Agents
  • RNA, Messenger
  • 1-(5-Isoquinolinesulfonyl)-2-Methylpiperazine
  • fasudil