Sturge-Weber Syndrome

Book
In: StatPearls [Internet]. Treasure Island (FL): StatPearls Publishing; 2023 Jan.
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Excerpt

Sturge-Weber syndrome (SWS) is a neurocutaneous syndrome characterized by angiomas involving the face, choroid, and leptomeninges. The facial capillary vascular malformation is also known as "port-wine stain" or "nevus flammeus" and usually is seen in the territory of the trigeminal nerve. Sturge-Weber syndrome is also called encephalotrigeminal angiomatosis. It is the third most common neurocutaneous syndrome after neurofibromatosis and tuberous sclerosis. The neurologic manifestations of SWS include atonic, tonic, or myoclonic seizures.

Publication types

  • Study Guide