Sturge-Weber Syndrome

In: StatPearls [Internet]. Treasure Island (FL): StatPearls Publishing; 2023 Jan.


Sturge-Weber syndrome (SWS) is a neurocutaneous syndrome characterized by angiomas involving the face, choroid, and leptomeninges. The facial capillary vascular malformation is also known as "port-wine stain" or "nevus flammeus" and usually is seen in the territory of the trigeminal nerve. Sturge-Weber syndrome is also called encephalotrigeminal angiomatosis. It is the third most common neurocutaneous syndrome after neurofibromatosis and tuberous sclerosis. The neurologic manifestations of SWS include atonic, tonic, or myoclonic seizures.

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  • Study Guide