Idiopathic Retinal Vasculitis, Aneurysms, and Neuroretinitis Syndrome Presenting With Branch Retinal Artery Occlusion

Ophthalmic Surg Lasers Imaging Retina. 2017 Nov 1;48(11):948-951. doi: 10.3928/23258160-20171030-13.

Abstract

Idiopathic retinal vasculitis, aneurysms, and neuroretinitis (IRVAN) is a rare syndrome affecting the retinal and optic disc vasculature. Diffuse retinal ischemia, macular edema, and neovascularization may lead to bilateral vision loss. The authors report a case of a 36-year-old woman presenting with branch retinal artery occlusion (BRAO) in her right eye who was subsequently diagnosed with IRVAN syndrome. She was treated with panretinal photocoagulation for peripheral retinal ischemia and pars plana vitrectomy for vitreous hemorrhage. She later developed a BRAO in her left eye. This case demonstrates that BRAO may be a presenting feature of IRVAN syndrome. [Ophthalmic Surg Lasers Imaging Retina. 2017;48:948-951.].

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Aneurysm / diagnosis*
  • Aneurysm / surgery
  • Female
  • Fluorescein Angiography
  • Humans
  • Laser Coagulation
  • Retinal Artery Occlusion / diagnosis*
  • Retinal Artery Occlusion / surgery
  • Retinal Vasculitis / diagnosis*
  • Retinal Vasculitis / surgery
  • Retinal Vessels / pathology*
  • Retinitis / diagnosis*
  • Retinitis / surgery
  • Tomography, Optical Coherence
  • Vitrectomy