Erythromelanosis follicularis faciei et colli: A clinicoepidemiologic study

Pediatr Dermatol. 2018 Jan;35(1):e70-e71. doi: 10.1111/pde.13322. Epub 2017 Nov 21.

Abstract

We describe 25 cases of erythromelanosis follicularis faciei et colli from India. The male:female ratio was 5.25:1 and the average age of onset was 12.3 years. The cheeks, preauricular area, and submandibular region were the sites most commonly affected. Keratosis pilaris was seen in 22 (88%) of the patients.

Keywords: erythromelanosis follicularis faciei et colli; follicular papules; hyperpigmentation; keratosis pilaris.

MeSH terms

  • Abnormalities, Multiple / diagnosis*
  • Abnormalities, Multiple / epidemiology
  • Adolescent
  • Child
  • Cross-Sectional Studies
  • Darier Disease / diagnosis*
  • Darier Disease / epidemiology
  • Diagnosis, Differential
  • Eyebrows / abnormalities*
  • Female
  • Humans
  • Hyperpigmentation / etiology
  • India
  • Male
  • Skin / pathology

Supplementary concepts

  • Burnett Schwartz Berberian syndrome