Abstract
Two cases of pulmonary lymphangioleiomyomatosis, with survival between 12 and 28 years are described. Both were treated with medroxyprogesterone acetate with a slight initial improvement in both lung function and exercise tolerance, and no further deterioration during the period of follow-up of 10-20 months. The results are discussed and other reports of hormonal treatment of this rare condition are reviewed.
MeSH terms
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Adult
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Female
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Follow-Up Studies
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Humans
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Lung / physiopathology
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Lung Neoplasms / drug therapy*
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Lung Neoplasms / physiopathology
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Lymphangiomyoma / drug therapy*
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Lymphangiomyoma / physiopathology
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Lymphoproliferative Disorders / drug therapy*
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Medroxyprogesterone / analogs & derivatives*
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Medroxyprogesterone / therapeutic use
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Medroxyprogesterone Acetate
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Respiratory Function Tests
Substances
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Medroxyprogesterone Acetate
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Medroxyprogesterone