Cerebrovascular disorders and Fahr's disease: Report of two cases and literature review

J Clin Neurosci. 2018 Apr;50:163-164. doi: 10.1016/j.jocn.2018.01.002. Epub 2018 Feb 1.


Fahr's disease is a rare idiopathic nosological entity, characterized by calcification of the basal ganglia and dentate nuclei of the cerebellum. Sometimes it may be associated to other diseases like cerebrovascular disorders. However, this link remains unclear and it needs to be further validated. We report two cases of patients with cerebrovascular disorders and Fahr's disease. In the first case, a 69-years-old woman with right internal capsule-basal ganglia haemorrhage. In the second case, a 72-years-old woman with ischemic stroke and pericallosal artery aneurysm. The physiopathology is discussed and concerning literature is reviewed.

Keywords: Fah'r disease; Idiopathic basal ganglia calcification; Intracranial haemorrhage; Pericallosal artery aneurysm; Stroke.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Aged
  • Basal Ganglia Diseases / complications*
  • Basal Ganglia Hemorrhage / etiology*
  • Calcinosis / complications*
  • Cerebrovascular Disorders / etiology
  • Female
  • Humans
  • Intracranial Aneurysm / etiology*
  • Neurodegenerative Diseases / complications*
  • Stroke / etiology*

Supplementary concepts

  • Fahr's disease