Diagnosing Tongue Base Obstruction in Pierre Robin Sequence Infants: Sleep vs Awake Endoscopy

Cleft Palate Craniofac J. 2018 May;55(5):692-696. doi: 10.1177/1055665618756706. Epub 2018 Feb 15.

Abstract

Objective: To investigate whether awake endoscopy can diagnose base-of-tongue obstruction as reliably as sleep endoscopy in infants with Pierre Robin sequence (PRS).

Design: The study was retrospective with the clinicians blinded to patient identity. Endoscopy findings were assessed and measured by the performing pediatric otolaryngologist.

Setting: Tertiary care children's hospital.

Patients: All infants with PRS managed between January 2005 and July 2015 were included. There were 141 patients, of which 35 underwent both awake endoscopy (AE) and drug-induced sleep endoscopy (DISE).

Interventions: Bedside AE and DISE in the operating room.

Main outcome measures: Presence of moderate or severe base-of-tongue collapse was assessed. Sensitivity, specificity, and positive likelihood ratio of AE findings as well as intertest differences between AE and DISE were calculated.

Results: AE had 50.0% sensitivity (95% confidence interval [CI] 27.2%-72.8%) and 86.7% specificity (95% CI 59.5%-98.3%) for detecting base-of-tongue obstruction compared to DISE; false negative rate was 50.0% (n = 10). Positive likelihood ratio was 3.75 (CI 0.96-14.65). Compared to AE, DISE demonstrated significantly more cases of base-of-tongue obstruction ( P = .039).

Conclusions: Bedside AE has low sensitivity for detecting base-of-tongue collapse in infants with PRS. Because of the substantial false negative rate, AE may not be a reliable diagnostic modality for ruling out base-of-tongue obstruction in this susceptible population. DISE may be indicated in high-risk patients to avoid underdiagnosing upper airway obstruction.

Keywords: Pierre Robin sequence; airway obstruction; endoscopy; nasopharyngoscopy; pediatrics; sleep disorders; tongue.

MeSH terms

  • Airway Obstruction / diagnosis*
  • Anesthetics, Inhalation / administration & dosage*
  • Anesthetics, Intravenous / administration & dosage*
  • Endoscopy / methods*
  • Female
  • Humans
  • Infant
  • Infant, Newborn
  • Male
  • Pierre Robin Syndrome / diagnosis*
  • Propofol / administration & dosage*
  • Retrospective Studies
  • Sensitivity and Specificity
  • Sevoflurane / administration & dosage*
  • Single-Blind Method
  • Sleep Apnea, Obstructive / diagnosis*
  • Tongue / abnormalities*

Substances

  • Anesthetics, Inhalation
  • Anesthetics, Intravenous
  • Sevoflurane
  • Propofol