Guidelines on the Diagnosis and Treatment of Pulmonary Hypertension: Summary of Recommendations

Arch Bronconeumol (Engl Ed). 2018 Apr;54(4):205-215. doi: 10.1016/j.arbres.2017.11.014. Epub 2018 Feb 19.
[Article in English, Spanish]


Pulmonary hypertension is a hemodynamic disorder defined by abnormally high pulmonary artery pressure that can occur in numerous diseases and clinical situations. The causes of pulmonary hypertension are classified into 5 major groups: arterial, due to left heart disease, due to lung disease and/or hypoxemia, chronic thromboembolic, with unclear and/or multifactorial mechanisms. This is a brief summary of the Guidelines on the Diagnostic and Treatment of Pulmonary Hypertension of the Spanish Society of Pulmonology and Thoracic Surgery. These guidelines describe the current recommendations for the diagnosis and treatment of the different pulmonary hypertension groups.

Keywords: Chronic thromboembolic pulmonary hypertension; Circulación pulmonar; Clinical guidelines; Guía clínica; Hipertensión arterial pulmonar; Hipertensión pulmonar; Hipertensión pulmonar tromboembólica crónica; Pulmonary arterial hypertension; Pulmonary circulation; Pulmonary hypertension.

Publication types

  • Practice Guideline

MeSH terms

  • Algorithms
  • Combined Modality Therapy
  • Connective Tissue Diseases / complications
  • Connective Tissue Diseases / diagnosis
  • Diagnostic Techniques, Cardiovascular / standards
  • Diagnostic Techniques, Respiratory System / standards
  • Disease Management
  • Drug Therapy, Combination
  • Evidence-Based Medicine
  • Heart Defects, Congenital / complications
  • Heart Diseases / complications
  • Heart Diseases / diagnosis
  • Heart Septum / surgery
  • Hospital Units / organization & administration
  • Humans
  • Hypertension, Pulmonary / classification
  • Hypertension, Pulmonary / diagnosis*
  • Hypertension, Pulmonary / etiology
  • Hypertension, Pulmonary / therapy*
  • Lung Transplantation
  • Metabolic Diseases / complications
  • Mutation
  • Oxygen Inhalation Therapy
  • Referral and Consultation / organization & administration
  • Respiration Disorders / complications