Life-threatening hemoptysis: case of Osler-Weber-Rendu Syndrome

Oxf Med Case Reports. 2018 Mar 22;2018(3):omx108. doi: 10.1093/omcr/omx108. eCollection 2018 Mar.

Abstract

Hereditary haemorrhagic telangiectasia (HHT), also known as Osler-Weber-Rendu syndrome, is a rare autosomal dominant vascular disorder. Patients with HHT may present with a wide spectrum of clinical manifestations, some considered to be life-threatening. We present the case of a 53-year-old male who presented with massive haemoptysis. Chest computed tomography scan was remarkable for a large anterior, left lower lobe arteriovenous malformation. The patient underwent a pulmonary angiogram with embolization of a large left lung arteriovenous malformation, which proved to be successful in controlling the bleeding.

Publication types

  • Case Reports