Catastrophic multiple arterial dissections revealing concomitant polyarteritis nodosa and vascular Elhers-Danlos syndrome

Clin Exp Rheumatol. 2018 Mar-Apr;36 Suppl 111(2):174-175. Epub 2018 May 3.
No abstract available

Publication types

  • Case Reports
  • Letter

MeSH terms

  • Adult
  • Aneurysm, Ruptured / complications
  • Aneurysm, Ruptured / physiopathology
  • Carotid Arteries / diagnostic imaging
  • Carotid Arteries / physiopathology
  • Carotid Artery Diseases / diagnostic imaging
  • Carotid Artery Diseases / etiology
  • Carotid Artery Diseases / physiopathology*
  • Cavernous Sinus / diagnostic imaging
  • Cavernous Sinus / physiopathology
  • Collagen Type III / genetics
  • Compartment Syndromes / physiopathology
  • Dilatation, Pathologic / diagnostic imaging
  • Dilatation, Pathologic / etiology
  • Dilatation, Pathologic / physiopathology*
  • Ehlers-Danlos Syndrome / complications
  • Ehlers-Danlos Syndrome / diagnostic imaging
  • Ehlers-Danlos Syndrome / genetics
  • Ehlers-Danlos Syndrome / physiopathology*
  • Female
  • Humans
  • Iliac Artery / diagnostic imaging
  • Iliac Artery / physiopathology
  • Infarction / diagnostic imaging
  • Infarction / etiology
  • Infarction / physiopathology
  • Mesenteric Artery, Superior / diagnostic imaging
  • Mesenteric Artery, Superior / physiopathology
  • Mutation
  • Polyarteritis Nodosa / complications
  • Polyarteritis Nodosa / diagnostic imaging
  • Polyarteritis Nodosa / physiopathology*
  • Renal Artery / diagnostic imaging
  • Renal Artery / physiopathology
  • Thrombosis / diagnostic imaging
  • Thrombosis / etiology
  • Thrombosis / physiopathology
  • Ulnar Artery / physiopathology
  • Vascular Fistula / diagnostic imaging
  • Vascular Fistula / etiology
  • Vascular Fistula / physiopathology*

Substances

  • COL3A1 protein, human
  • Collagen Type III