Effect of LGI1 antibody-positive IgG on hippocampal neuron survival: a preliminary study

Neuroreport. 2018 Aug 1;29(11):932-938. doi: 10.1097/WNR.0000000000001055.

Abstract

Anti-leucine-rich glioma inactivated 1 (anti-LGI1) encephalitis is one of the most frequently encountered forms of autoimmune encephalitis. Many patients with anti-LGI1 encephalitis develop permanent hippocampal neuron loss and chronic neuropsychiatric symptoms, suggesting that LGI antibodies (Ab) might have a neurotoxic action. To investigate this hypothesis, purified serum IgG of three patients with anti-LGI1 encephalitis and six healthy controls were incubated with cultured primary hippocampal neurons obtained from newborn mice. Nontreated cells were used as controls. The viability of IgG-treated neurons was evaluated by propidium iodide staining. Apoptotic mechanisms were assessed by JC-1 assay and mRNA expression level measurement of apoptosis-related genes using real-time PCR. The effect of IgG treatment on calcium influx was analyzed by fluo-4 calcium imaging. LGI1-Ab+ IgG increased the number of propidium iodide positive neurons, reduced mitochondrial membrane potentials, upregulated caspase-3 and Bax mRNA expression levels and downregulated Bcl-2 mRNA expression levels of neurons. LGI1-Ab+ IgG-treated neurons showed lower calcium staining than healthy controls IgG-treated and non-IgG-treated neurons. Our results indicate a neurotoxic role of LGI1-Ab. This neurotoxicity is likely mediated through induction of apoptosis and reduction of calcium currents.

MeSH terms

  • Animals
  • Autoantibodies / metabolism*
  • Extracellular Space / metabolism
  • Hippocampus / metabolism*
  • Immunoglobulin G / immunology*
  • Intracellular Signaling Peptides and Proteins
  • Membrane Proteins / metabolism
  • Mice
  • Mice, Inbred BALB C
  • Nerve Tissue Proteins / metabolism
  • Neurons / immunology
  • Neurons / metabolism*
  • Potassium Channels, Voltage-Gated / metabolism
  • Proteins / immunology*

Substances

  • Autoantibodies
  • Immunoglobulin G
  • Intracellular Signaling Peptides and Proteins
  • Lgi1 protein, mouse
  • Membrane Proteins
  • Nerve Tissue Proteins
  • Potassium Channels, Voltage-Gated
  • Proteins