Atypical Maculopapular Cutaneous Mastocytosis Showing a Nevus Spilus-Like Lesion

Pediatr Dermatol. 2018 Sep;35(5):e306-e307. doi: 10.1111/pde.13541. Epub 2018 Jun 22.


A 13-year-old Korean girl presented with a 7-year history of a pruritic, light-brown patch containing multiple 0.2- to 0.5-cm brownish-to-reddish maculopapules on the left anterior chest. When her skin was rubbed, the lesion became itchy and red. Histopathologic evaluation demonstrated marked dense dermal infiltration of mast cells. We report a rare case of atypical maculopapular cutaneous mastocytosis with clinical features similar to those of nevus spilus.

Keywords: mastocytosis; neoplasm-benign; pigmentary disorder.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Diagnosis, Differential
  • Female
  • Humans
  • Nevus / pathology
  • Skin / pathology*
  • Urticaria Pigmentosa / diagnosis
  • Urticaria Pigmentosa / pathology*