Right Heart-Pulmonary Circulation Unit in Congenital Heart Diseases

Heart Fail Clin. 2018 Jul;14(3):283-295. doi: 10.1016/j.hfc.2018.02.005.


The right ventricle plays a major role in congenital heart disease. This article describes the right ventricular mechanics in some selected congenital heart diseases affecting the right ventricle in different ways: tetralogy of Fallot, Ebstein anomaly, and the systemic right ventricle.

Keywords: Congenital heart disease; Ebstein anomaly; Right ventricle; Tetralogy of Fallot.

Publication types

  • Review

MeSH terms

  • Echocardiography / methods
  • Heart Defects, Congenital / physiopathology*
  • Heart Defects, Congenital / surgery
  • Heart Ventricles / diagnostic imaging
  • Heart Ventricles / physiopathology*
  • Humans
  • Magnetic Resonance Imaging, Cine / methods
  • Pulmonary Circulation / physiology*
  • Ventricular Dysfunction, Right / diagnostic imaging
  • Ventricular Dysfunction, Right / etiology*