Definition and Management of Segmental Pulmonary Hypertension

Konstantinos Dimopoulos; Gerhard-Paul Diller; Alexander R Opotowsky; Michele D'Alto; Hong Gu; George Giannakoulas; Werner Budts; Craig S Broberg; Gruschen Veldtman; Lorna Swan; Maurice Beghetti; Michael A Gatzoulis

doi:10.1161/JAHA.118.008587

Definition and Management of Segmental Pulmonary Hypertension

J Am Heart Assoc. 2018 Jul 4;7(14):e008587. doi: 10.1161/JAHA.118.008587.

Authors

Affiliations

¹ Adult Congenital Heart Centre and National Centre for Pulmonary Hypertension, Biomedical Research Unit, National Heart and Lung Institute Royal Brompton Hospital Imperial College, London, United Kingdom k.dimopoulos02@gmail.com.
² Division of Adult Congenital and Valvular Heart Disease, Department of Cardiovascular Medicine, University Hospital Muenster, Muenster, Germany.
³ Boston Adult Congenital Heart (BACH) and Pulmonary Hypertension Group, Boston Children's Hospital and Brigham and Women's Hospital Harvard Medical School, Boston, MA.
⁴ Department of Cardiology, Monaldi di Hospital - Second University of Naples, Italy.
⁵ Beijing Anzhen Hospital Capital Medical University, Beijing, China.
⁶ First Department of Cardiology, AHEPA University Hospital Aristotle University of Thessaloniki, Greece.
⁷ Congenital and Structural Cardiology, University Hospitals Leuven, Leuven, Belgium.
⁸ Department of Cardiovascular Sciences, Catholic University Leuven, Leuven, Belgium.
⁹ Knight Cardiovascular Institute Oregon Health and Science University, Portland, OR.
¹⁰ Heart Institute, Cincinnati Children's Hospital Medical Center, Cincinnati, OH.
¹¹ Adult Congenital Heart Centre and National Centre for Pulmonary Hypertension, Biomedical Research Unit, National Heart and Lung Institute Royal Brompton Hospital Imperial College, London, United Kingdom.
¹² Paediatric Cardiology Unit, University Hospital of Geneva, Switzerland.
¹³ Centre Universitaire Romand de Cardiologie et Chirurgie Cardiaque Pédiatrique University of Lausanne, Geneva, Switzerland.

No abstract available

Keywords: congenital heart disease; pulmonary atresia; pulmonary hypertension; segmental pulmonary hypertension; truncus arteriosus.

Publication types

Consensus Development Conference

MeSH terms

Bosentan / therapeutic use
Cardiac Surgical Procedures / methods
Disease Management
Endothelin Receptor Antagonists / therapeutic use
Heart Defects, Congenital / complications
Heart Defects, Congenital / physiopathology*
Heart Defects, Congenital / surgery
Humans
Hypertension, Pulmonary / classification*
Hypertension, Pulmonary / etiology
Hypertension, Pulmonary / physiopathology
Hypertension, Pulmonary / therapy
Vascular Malformations / complications
Vascular Malformations / physiopathology*

Substances

Endothelin Receptor Antagonists
Bosentan