Noninvasive ventilatory support to reverse weight loss in Duchenne muscular dystrophy: A case series

Pulmonology. 2019 Mar-Apr;25(2):79-82. doi: 10.1016/j.pulmoe.2018.06.002. Epub 2018 Jul 19.

Abstract

This case series of five patients with Duchenne muscular dystrophy demonstrates the nutritional advantages of instituting noninvasive intermittent positive pressure ventilatory support via 15mm angled mouthpieces to relieve tachypnea and provide more time to swallow food safely. In each case weight loss was reversed.

Keywords: Duchenne muscular dystrophy; Dysphagia; Malnutrition; Neuromuscular disease; Noninvasive ventilation; Noninvasive ventilatory support.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Adult
  • Deglutition / physiology
  • Deglutition Disorders / physiopathology
  • Fatal Outcome
  • Humans
  • Male
  • Malnutrition / etiology
  • Middle Aged
  • Muscular Dystrophy, Duchenne / complications
  • Muscular Dystrophy, Duchenne / therapy*
  • Noninvasive Ventilation / methods*
  • Positive-Pressure Respiration / instrumentation*
  • Tachypnea / complications
  • Tachypnea / physiopathology
  • Tracheotomy / adverse effects
  • Weight Loss / physiology*
  • Young Adult