Hepatocellular carcinoma associated with arteriohepatic dysplasia

Dig Dis Sci. 1986 Apr;31(4):438-42. doi: 10.1007/BF01311683.


This report documents the occurrence of hepatocellular carcinoma in a 36-year-old man with arteriohepatic dysplasia and a noncirrhotic liver. This case represents one of the oldest patients reported to have arteriohepatic dysplasia and the first with the development of a hepatocellular carcinoma, of which I am aware. Although this tumor has been reported with other familial cholestatic syndromes, the absence of an underlying cirrhosis is of particular interest.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Bile Ducts, Intrahepatic / abnormalities
  • Carcinoma, Hepatocellular / etiology*
  • Cholestasis, Intrahepatic / complications
  • Cholestasis, Intrahepatic / congenital*
  • Cornea / abnormalities
  • Face / abnormalities
  • Humans
  • Liver Neoplasms / etiology*
  • Male
  • Syndrome