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, 20 (1), 76-81

Chronic Inflammatory Demyelinating Polyneuropathy of Infancy: A Corticosteroid-Responsive Disorder

Chronic Inflammatory Demyelinating Polyneuropathy of Infancy: A Corticosteroid-Responsive Disorder

J T Sladky et al. Ann Neurol.

Abstract

We present the clinical, electrophysiological, and histopathological findings in 6 children with early-onset chronic inflammatory demyelinating neuropathy. The clinical features initially suggested a genetically determined disorder in each patient. Sural nerve biopsy showed changes of chronic demyelination with multifocal endoneurial edema and mononuclear cellular infiltrates. All children improved with corticosteroid therapy.

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