Management of congenital ichthyoses: European guidelines of care, part one

Br J Dermatol. 2019 Feb;180(2):272-281. doi: 10.1111/bjd.17203. Epub 2018 Dec 3.

Abstract

These guidelines for the management of congenital ichthyoses have been developed by a multidisciplinary group of European experts following a systematic review of the current literature, an expert conference held in Toulouse in 2016 and a consensus on the discussions. They summarize evidence and expert-based recommendations and are intended to help clinicians with the management of these rare and often complex diseases. These guidelines comprise two sections. This is part one, covering topical therapies, systemic therapies, psychosocial management, communicating the diagnosis and genetic counselling.

Publication types

  • Practice Guideline

MeSH terms

  • Administration, Oral
  • Administration, Topical
  • Behavior Therapy / methods
  • Behavior Therapy / standards*
  • Consensus*
  • Dermatologic Agents / therapeutic use*
  • Dermatology / methods
  • Dermatology / standards*
  • Europe
  • Genetic Counseling / standards
  • Humans
  • Ichthyosiform Erythroderma, Congenital / diagnosis
  • Ichthyosiform Erythroderma, Congenital / psychology
  • Ichthyosiform Erythroderma, Congenital / therapy*
  • Quality of Life
  • Social Support
  • Systematic Reviews as Topic

Substances

  • Dermatologic Agents