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. 2018 Jan;6(1):e77-e80.
doi: 10.1055/s-0038-1672147. Epub 2018 Oct 18.

Chronic Urinary Retention Due to Fowler's Syndrome

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Free PMC article
Case Reports

Chronic Urinary Retention Due to Fowler's Syndrome

Jan Trachta et al. European J Pediatr Surg Rep. .
Free PMC article

Abstract

Fowler's syndrome (FS) is a rare cause of chronic urinary retention in teenage girls and young women. We present a case of a 14-year-old girl who presented at our hospital 2 weeks after uncomplicated laparoscopic appendectomy. The girl complained of reduced urinary frequency and prolonged micturition time. Following an acute cystitis 2 months later, she completely lost her ability to void. A comprehensive set of investigations to assess the cause of her urinary retention including a cerebral and spinal magnetic resonance imaging (MRI), and videourodynamics were performed. The diagnostic workup revealed polycystic ovaries and an asensitive and hypotonic bladder with capacity up to 1200 mL and high maximum urethral pressure of 120 cm of water. She did not tolerate clean intermittent catheterization; therefore, a suprapubic catheter was placed. Under this treatment, she suffered recurrent urinary tract infections. Two years later, she was diagnosed with FS on the basis of the medical history, clinical symptoms, and urodynamic findings. Finally, the implantation of a S3 neurostimulator restored her ability to void.

Keywords: Fowler's syndrome; sacral neuromodulation; urinary retention.

Conflict of interest statement

Conflict of Interest None.

Figures

Fig. 1
Fig. 1
Normal looking bladder on videourodynamic study.
Fig. 2
Fig. 2
Wounds after bilateral S3 neurostimulator implantation.
Fig. 3
Fig. 3
Transcutaneous remote control of current intensity of the S3 neurostimulators.

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References

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