Intramedullary spinal cord tumours (IMSCT) are rare neoplasms, which can potentially lead to severe neurologic deficits. In this case report, an 83-year-old man presented with rapidly progressive bilateral muscle weakness developed within few weeks. MRI revealed a spinal cord tumour at the C7/Th1 vertebral level. Surgical resection was performed, and the histological diagnosis was subependymoma. Focus on IMSCT as a differential diagnosis is important, since early diagnosis and treatment will pave the way for a better prognosis.