Atrioventricular Canal and Dextrocardia: A Case Report with Implications for Community-Based Providers

Neonatal Netw. 2018 Sep;37(5):281-291. doi: 10.1891/0730-0832.37.5.281. Epub 2018 Sep 1.

Abstract

Congenital heart defects (CHD) are the most common congenital malformation reported in the literature, with a global incidence of eight per every 1,000 live births. In the United States approximately 40,000 infants are born each year with a CHD. Of the infants diagnosed with a CHD, one in every four heart defects are life threatening in origin. Early identification and treatment of congenital heart lesions, beginning with a comprehensive physical assessment after birth, are critical. For infants delivered at community-based hospitals, the importance of the physical assessment, timing of diagnostic strategies, anticipatory planning, and interprofessional collaboration among referring and accepting centers cannot be understated. This article presents a rare case of an infant with atrioventricular canal complicated by dextrocardia. Embryology, pathophysiology, epidemiology, symptomology, cardiac assessment, diagnostics, treatment, and nursing strategies for facilitating transfer of care from community-based hospitals to tertiary medical centers are discussed.

Keywords: atrioventricular canal; cardiac anomalies; cardiac assessment; cardiology; congenital heart defects; dextrocardia; embryology; heart; neonatal/infant; newborn; physical assessment.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Dextrocardia / diagnosis
  • Dextrocardia / epidemiology
  • Dextrocardia / physiopathology*
  • Dextrocardia / surgery*
  • Heart Defects, Congenital / diagnosis
  • Heart Defects, Congenital / physiopathology*
  • Heart Defects, Congenital / surgery*
  • Heart Septal Defects / diagnosis
  • Heart Septal Defects / epidemiology
  • Heart Septal Defects / physiopathology*
  • Heart Septal Defects / surgery*
  • Humans
  • Incidence
  • Infant, Newborn
  • Male
  • Treatment Outcome
  • United States / epidemiology

Supplementary concepts

  • Atrioventricular Septal Defect