Ligneous conjunctivitis in a Dandy-Walker syndrome: A rare case report

Indian J Ophthalmol. 2019 Jan;67(1):143-145. doi: 10.4103/ijo.IJO_772_18.

Abstract

Ligneous conjunctivitis (LC) is a rare form of pseudomembranous conjunctivitis seen in children, perhaps due to plasminogen deficiency, which manifest as a chronic refractory pseudomembranous conjunctivitis. LC cases are incapable in maintaining their fibrinolytic activity due to plasminogen deficiency; consequently, transudates of plasma assume as a thick, gelatinous, woody membranes over the mucosal surfaces. This is a short case report on a child with a LC, who presented with recurrent pseudomembranous conjunctivitis in conjunction with progressive congenital hydrocephalus due to aqueductal stenosis (Dandy-Walker syndrome). This rare association was clinically confirmed and prompt corrective surgical measures were instituted.

Keywords: Dandy–Walker syndrome; hydrocephalus; ligneous conjunctivitis.

Publication types

  • Case Reports

MeSH terms

  • Conjunctiva / pathology*
  • Conjunctivitis / diagnosis
  • Conjunctivitis / etiology*
  • Dandy-Walker Syndrome / complications*
  • Dandy-Walker Syndrome / diagnosis
  • Humans
  • Infant
  • Male
  • Rare Diseases
  • Tomography, X-Ray Computed