An anesthetic experience in a patient with Seckel syndrome: A case report

Korean J Anesthesiol. 2009 Feb;56(2):204-207. doi: 10.4097/kjae.2009.56.2.204.

Abstract

Seckel syndrome is an autosomal recessive, primordial dwarfism. The clinical symptoms and signs include severe intrauterine and postnatal growth retardation, nanocephaly, proportional dwarfism, bird-like faces, beak-like triangular nose, and mental retardation. We report a successful anesthetic management including endotracheal intubation with the GlideScope(R) video laryngoscope in an 18-year old man with Seckel syndrome for curettage of chronic osteomyelitis of pelvic bone.

Keywords: Dwarfism; Endotracheal intubation; Nanocephaly; Seckel syndrome.