Guidelines for synoptic reporting of surgery and pathology in Hirschsprung disease

J Pediatr Surg. 2019 Oct;54(10):2017-2023. doi: 10.1016/j.jpedsurg.2019.03.010. Epub 2019 Mar 21.


Background/purpose: Synoptic, or standardized, reporting of surgery and pathology reports has been widely adopted in surgical oncology. Patients with Hirschsprung disease may experience morbidity related to surgical factors or underlying pathology and often undergo multiple operations. Our aim is to improve the postoperative outcome and care of patients with Hirschsprung disease by proposing a standardized set of data that should be included in every surgery and pathology report.

Methods: Members of the American Pediatric Surgical Association Hirschsprung Disease Interest Group and experts in pediatric pathology of Hirschsprung disease participated in group discussions, performed literature review and arrived at expert consensus guidelines for surgery and pathology reporting.

Results: The importance of accurate operative and pathologic reports and the implications of inadequate documentation in patients with Hirschsprung disease are discussed and guidelines for standardizing these reports are provided.

Conclusions: Adherence to the principles of reporting for operations and surgical pathology may improve outcomes for Hirschsprung disease patients and will facilitate identification of correlations among morphology, function, genetics and outcomes, which are required to improve the overall management of these patients.

Level of evidence: V.

Keywords: Aganglionosis; Enteric nervous system; Hirschsprung disease; Pathology; Surgery; Synoptic.

Publication types

  • Review

MeSH terms

  • Digestive System Surgical Procedures / methods*
  • Enteric Nervous System / pathology*
  • Hirschsprung Disease / pathology
  • Hirschsprung Disease / surgery*
  • Humans
  • Practice Guidelines as Topic*