Moebius syndrome: The challenge of dental management

Eur J Paediatr Dent. 2019 Jun;20(2):143-146. doi: 10.23804/ejpd.2019.20.02.12.

Abstract

Aim: Moebius syndrome (MBS) is a rare disorder which involves unilateral or bilateral paralysis or lack of the VI and VII cranial nerves. This is accompanied by abnormalities affecting the head, mouth, upper and lower limbs, and chest. A distinguishing feature of this syndrome is the so-called mask-like face. A small number of publications relating to occlusal and dental bnormalities and documenting the progress of orthodontic treatment has led the authors to present the case of a patient with Moebius syndrome.

Case report: A patient with Moebius syndrome was initially treated by means of removable appliances and later by means of a fixed appliance after permanent tooth extractions. As a result of the treatment, there was an improvement in the ratio of the posterior facial height to the anterior facial height: Sgo/NGn increased from 55.8% to 59.1%, which is closer to the Caucasian population norm.

Conclusion: The aesthetic result was satisfactory both for the patient and for her parents.

MeSH terms

  • Face
  • Female
  • Humans
  • Mobius Syndrome*