Pediatric cerebral proliferative angiopathy presenting infratentorial hemorrhage

Childs Nerv Syst. 2020 Feb;36(2):429-433. doi: 10.1007/s00381-019-04313-x. Epub 2019 Jul 23.

Abstract

Cerebral proliferative angiopathies (CPAs) are distinct vascular malformations with varied clinical presentations and radiological findings from arteriovenous malformations (AVM) (Lasjaunias et al. in Stroke 39(3):878-85, 2008). They usually manifest with seizures if present supratentorial, headache, and progressive neurological deficits due to steal phenomenon or rarely with hemorrhage (Lasjaunias et al. in Stroke 39(3):878-85, 2008). Most of the patients are usually young females. Pediatric cases are extremely rare, with few cases reported till now. Here we report a child who presented with cerebellar bleed and diagnosed as CPA. The child was managed medically, and there was no change in caliber of the vessels after 18 months of follow-up. A short review of cases of CPA in pediatric age group presentations and management was undertaken in this case report.

Keywords: AVM; Cerebral proliferative angiopathy; Infratentorial hemorrhage.

Publication types

  • Case Reports

MeSH terms

  • Cerebellar Diseases*
  • Cerebral Angiography
  • Cerebral Hemorrhage / diagnostic imaging
  • Cerebral Hemorrhage / etiology
  • Child
  • Female
  • Headache
  • Humans
  • Intracranial Arteriovenous Malformations* / complications
  • Intracranial Arteriovenous Malformations* / diagnostic imaging