Bony Breathlessness: Reversible Pulmonary Hypertension in Melnick-Needles Syndrome Using Noninvasive Ventilation

Circulation. 2019 Sep 9;140(10):880-885. doi: 10.1161/CIRCULATIONAHA.119.040833. Epub 2019 Sep 3.

Authors

Beatrice Cockbain¹, Laura C Price², Matthew Hind³

Affiliations

¹ Department of Immunology and Infection, Barts Health NHS Trust, London, United Kingdom (B.C.).
² National Pulmonary Hypertension Service (L.C.P.), Royal Brompton Hospital, London, United Kingdom.
³ Department of Respiratory Medicine (M.H.), Royal Brompton Hospital, London, United Kingdom.

PMID: 31479319
DOI: 10.1161/CIRCULATIONAHA.119.040833

No abstract available

Keywords: dyspnea; hypertension, pulmonary; osteochondrodysplasias; syncope; ventricular dysfunction, right.

Publication types

Case Reports

MeSH terms

Asthma, Exercise-Induced
Dyspnea
Electrocardiography
Female
Filamins / genetics*
Humans
Hypertension, Pulmonary
Middle Aged
Noninvasive Ventilation / methods*
Osteochondrodysplasias / diagnosis
Osteochondrodysplasias / therapy*
Oximetry
Recovery of Function

Substances

FLNA protein, human
Filamins