[Successful detection of MYD88 L265P mutation in Waldenström's macroglobulinemia complicated with myelofibrosis using highly sensitive digital PCR]

Rinsho Ketsueki. 2019;60(8):903-909. doi: 10.11406/rinketsu.60.903.
[Article in Japanese]

Abstract

A 78-year-old man with anemia (Hb 9.6 g/dl) and elevated serum immunoglobulin M (IgM 3,577 mg/dl) levels was referred to our hospital. Bone marrow aspiration yielded a dry tap, and bone marrow biopsy revealed the infiltration of CD20 positive lymphoplasmacytic lymphoma cells and myelofibrosis. The patient was diagnosed with Waldenström's macroglobulinemia complicated with myelofibrosis. TGF-β plasma concentration was elevated. Further, after chemotherapy with bendamustine and rituximab, remission of both Waldenström's macroglobulinemia and myelofibrosis was achieved, and TGF-β levels normalized. MYD88 L265P mutation was detected using highly sensitive digital PCR, which compared with currently used direct PCR product sequencing, has a superior sensitivity. The use of digital PCR has additional advantages toward MYD88 L265P detection, particularly when the available amount of sample DNA is limited owing to myelofibrosis.

Keywords: Digital PCR; MYD88 L265P mutation; Myelofibrosis; Waldenström's macroglobulinemia (WM).

Publication types

  • Case Reports

MeSH terms

  • Aged
  • Humans
  • Immunoglobulin M
  • Male
  • Mutation
  • Myeloid Differentiation Factor 88 / genetics*
  • Polymerase Chain Reaction
  • Primary Myelofibrosis* / complications
  • Waldenstrom Macroglobulinemia* / complications
  • Waldenstrom Macroglobulinemia* / genetics

Substances

  • Immunoglobulin M
  • MYD88 protein, human
  • Myeloid Differentiation Factor 88