Single right coronary artery with right ventricular fistula and congenital absence of left coronary artery: an extremely rare combination

Cardiol Young. 2019 Nov;29(11):1402-1403. doi: 10.1017/S1047951119002105. Epub 2019 Sep 5.


We report an extremely rare case of a 14-month-old girl who was diagnosed with a single right coronary artery with coronary artery fistula communicating with the right ventricle and congenital absence of left coronary artery. Angiography showed a dilated and tortuous single right coronary artery draining into the right ventricle, absence of left coronary system, and left ventricular coronary circulation supplied via collateral vessels.

Keywords: Coronary artery fistula; coronary arteries anomalies; single coronary artery.

Publication types

  • Case Reports

MeSH terms

  • Abnormalities, Multiple*
  • Aortography
  • Cardiac Catheterization
  • Coronary Angiography
  • Coronary Vessel Anomalies / diagnosis*
  • Coronary Vessels / diagnostic imaging*
  • Female
  • Heart Ventricles / abnormalities*
  • Heart Ventricles / diagnostic imaging
  • Heart Ventricles / surgery
  • Humans
  • Infant
  • Rare Diseases
  • Vascular Fistula / diagnosis*