Scoliosis Correction with One Ventricle: A Multispecialty Approach

World Neurosurg. 2020 Feb;134:302-307. doi: 10.1016/j.wneu.2019.11.004. Epub 2019 Nov 9.


Background: Patients with single-ventricle congenital heart disease may present for scoliosis correction. These patients undergo a series of cardiac operations that create a novel circulation that has a significant impact on the management of their spinal surgery.

Case description: A 21-year-old man with severe scoliosis presented for posterior T4-L3 spinal fusion. He was born with complex congenital heart disease that resulted in his having a single functioning ventricle. He underwent a series of operations culminating in a Fontan procedure to palliate his heart disease. Both the surgical procedure and the anesthetic plan were modified based on his abnormal physiology, which led to a successful correction with no complications.

Conclusions: Patients who have undergone a Fontan procedure can successfully undergo a lengthy scoliosis correction, but it requires multidisciplinary planning.

Keywords: Fontan; Scoliosis; Single ventricle.

Publication types

  • Case Reports

MeSH terms

  • Fontan Procedure
  • Humans
  • Hypoplastic Left Heart Syndrome / complications*
  • Hypoplastic Left Heart Syndrome / surgery
  • Male
  • Scoliosis / complications*
  • Scoliosis / surgery*
  • Spinal Fusion / methods*
  • Young Adult