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Case Reports
. Jul-Dec 2019;10(2):241-244.
doi: 10.4103/njms.NJMS_67_18. Epub 2019 Nov 12.

A Rare Case of Bilateral Oblique Facial Cleft and Accessory Maxilla With Repaired Unilateral Cleft Lip and Palate

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Free PMC article
Case Reports

A Rare Case of Bilateral Oblique Facial Cleft and Accessory Maxilla With Repaired Unilateral Cleft Lip and Palate

Veerendra Prasad et al. Natl J Maxillofac Surg. .
Free PMC article

Abstract

Cleft lip and palate (CLP) are commonly occurring birth defects which occur due to failure of fusion of various developmental processes of the face, leading to a visible defect in the lip and palate. In severe cases, this defect may extend over the face, thus causing facial clefts. The present case of a 7-year-old girl is unique in the sense that she has right and left side facial clefts of different severity with bilateral accessory maxilla, extra set of dentition, unilateral CLP of the right side, and a double soft palate. Other less associated findings in the case are severe maxillary protrusion, complex open bite, downward and backward rotation of mandible, and incompetent lips with apparently no limb deformities. With some relevant data in hand, we present this case for various suggestions and best possible treatment plan.

Keywords: Accessory maxilla; open bite; orofacial cleft; unilateral cleft lip and palate.

Conflict of interest statement

There are no conflicts of interest.

Figures

Figure 1
Figure 1
Pretreatment extraoral photographs
Figure 2
Figure 2
Pretreatment intraoral photographs
Figure 3
Figure 3
Cone-beam computed tomography – three-dimensional reconstruction of the skull
Figure 4
Figure 4
Lateral cephalogram showing Class II pattern with open bite and protrusive maxilla
Figure 5
Figure 5
Normal hands and feet
Figure 6
Figure 6
Axial view of cone-beam computed tomography section showing two sets of accessory posterior dentition on the accessory maxilla
Figure 7
Figure 7
Panoramic radiograph

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References

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