Long-Term Management and Maxillofacial Growth in a Klippel-Trenaunay Syndrome Patient

Cleft Palate Craniofac J. 2020 Jun;57(6):782-790. doi: 10.1177/1055665619895863. Epub 2019 Dec 26.

Abstract

Klippel-Trenaunay syndrome (KTS) is a congenital disorder associated with capillary, venous, lymphatic vascular malformations, and unilateral hypertrophy of the soft tissue and bone. We report a case of a 5-year-old girl with KTS who was followed up until age 17. The asymmetry of her maxillary dentition became remarkable with growth, although no significant left-right difference in either the maxilla or mandible was recognized. Acceptable occlusion was achieved without fixed orthodontic appliances; however, it was necessary to develop treatment plans in accordance with the general symptoms of the disease.

Keywords: Klippel-Trenaunay syndrome; long-term management; maxillofacial growth.

Publication types

  • Case Reports

MeSH terms

  • Child, Preschool
  • Female
  • Humans
  • Klippel-Trenaunay-Weber Syndrome* / diagnostic imaging
  • Klippel-Trenaunay-Weber Syndrome* / therapy
  • Mandible / diagnostic imaging
  • Patients