Ciliary Localization of the Intraflagellar Transport Protein IFT88 Is Disrupted in Cystic Fibrosis

Am J Respir Cell Mol Biol. 2020 Jan;62(1):120-123. doi: 10.1165/rcmb.2018-0287LE.
No abstract available

Publication types

  • Letter
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Adult
  • Child
  • Child, Preschool
  • Cilia / metabolism*
  • Cystic Fibrosis / metabolism*
  • Female
  • Humans
  • Inflammation / metabolism
  • Male
  • Middle Aged
  • Protein Transport / physiology*
  • Tumor Suppressor Proteins / metabolism*
  • Young Adult

Substances

  • IFT88 protein, human
  • Tumor Suppressor Proteins