Presentation of Infantile Hemangiopericytoma/Solitary Fibrous Tumor as a Giant Extracranial Temporal Mass

Fetal Pediatr Pathol. 2021 Oct;40(5):523-527. doi: 10.1080/15513815.2020.1716904. Epub 2020 Jan 29.


Infantile Hemangiopericytoma (HPC)/Solitary Fibrous Tumor (SFT), a vascular tumor of head and neck region, can be congenital or arise during the first year of the life. As the infantile form of hemangiopericytoma has a better course than the adult form, surgical excision is recommended. Case Report: A full-term neonate presented with a congenital right temporal soft tissue mass. MRI revealed a highly vascular mass with a hemorrhagic and possible necrotic core without intracranial extension. The lesion grew in 2 weeks from 4x4 cm to 9x7 cm. Histologically, a hypercellular spindle cell mesenchymal neoplasm had prominent staghorn vessels, alternating with hypocellular areas. Mitotic activity was low(1-3/HPF) and necrosis was absent. Conclusion: Infantile HPC/SFT of head and neck can grow rapidly during the infantile period. Complete excision without mutilating surgery should be curative.

Keywords: Infantile hemangiopericytoma; extracranial; temporal mass.

Publication types

  • Case Reports

MeSH terms

  • Hemangiopericytoma* / diagnosis
  • Hemangiopericytoma* / surgery
  • Humans
  • Infant, Newborn
  • Solitary Fibrous Tumors* / diagnosis
  • Solitary Fibrous Tumors* / surgery