Intraocular Lens Dislocation into the Anterior Chamber because of Repeated Eye-Poking in a Patient with Leber's Congenital Amaurosis

Abdullah A Al-Owaid; Motazz A Alarfaj; Faris A Alarfaj; Abdulaziz Awad

doi:10.1159/000505596

Intraocular Lens Dislocation into the Anterior Chamber because of Repeated Eye-Poking in a Patient with Leber's Congenital Amaurosis

Case Rep Ophthalmol. 2020 Jan 22;11(1):48-53. doi: 10.1159/000505596. eCollection 2020 Jan-Apr.

Authors

Abdullah A Al-Owaid^{1

2}, Motazz A Alarfaj^{1

2}, Faris A Alarfaj^{1

2}, Abdulaziz Awad¹

Affiliations

¹ King Khaled Eye Specialist Hospital, Riyadh, Saudi Arabia.
² Department of Ophthalmology, College of Medicine, Imam Abdulrahman Bin Faisal University, Dammam, Saudi Arabia.

Abstract

The dislocation of a posterior chamber intraocular lens (PC IOL) because of constant eye rubbing is unusual and has never been reported in a child with Leber's congenital amaurosis (LCA). A 4-year-old full-term girl with an ocular history of LCA presented to the emergency room with a single-piece PC IOL dislocated into the anterior chamber (AC) of the left eye. There was no history of trauma or any other surgical intervention. A specific behavior known as Franceschetti's oculo-digital sign is a characteristic feature of LCA; this sign consists of repeated pressing, poking, and rubbing of the eyes with knuckles and fingers to stimulate the photoreceptors. This behavior caused the dislocation of the PC IOL into the AC. The dislocated IOL was explanted, and the patient was provided with aphakic glasses.

Keywords: Dislocated IOL; Eye rubbing; Leber's congenital amaurosis; Retinal dystrophy.

Publication types

Case Reports