Diagnosis and management of the adult patient with a failing Fontan circulation

Heart Fail Rev. 2020 Jul;25(4):633-646. doi: 10.1007/s10741-020-09932-0.


Since the original description, the Fontan operation has been widely used for the palliation of children with single ventricle physiology. Although the Fontan operation revolutionized the survival rates of patients with single ventricle physiology, it carries an inevitable risk for long-term morbidity and mortality that impacts clinical outcomes and quality of life. This review will focus on the evaluation and treatment of the patient with the failing Fontan phenotype, with an emphasis on creating an individualized treatment plan.

Keywords: Congenital heart disease; Fontan; Heart failure; Single ventricle.

Publication types

  • Review

MeSH terms

  • Adult
  • Diagnostic Imaging / methods*
  • Disease Management*
  • Fontan Procedure / methods*
  • Heart Defects, Congenital / diagnosis*
  • Heart Defects, Congenital / surgery
  • Humans
  • Palliative Care / methods*